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IgG4-related retroperitoneal fibrosis: A case report and review of literature
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نویسنده
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niaz a. ,ahmad a.h. ,rahman k.-u. ,saeed m.a. ,sabir o. ,tarif n.
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منبع
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journal of the pakistan medical association - 2016 - دوره : 66 - شماره : 2 - صفحه:220 -222
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چکیده
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Idiopathic retroperitoneal fibrosis is a rare clinical condition recently identified as an autoimmune process related to immunoglobulin g4 (igg4) deposition. herein we report a case of a 46 year old male presenting with 4 months history of backache,fever,flank pain and leg swelling for 2 weeks. investigations revealed acute kidney injury diagnosed as a result of bilateral ureteric obstruction. this was later confirmed to be retroperitoneal fibrosis on ct scan and biopsy. histopathology was consistent with igg4 related disease. treatment with immunosuppressive agents showed reduction in the fibrosis and normalization of the kidney functions. we discuss the igg4 related retroperitoneal fibrosis in detail along with its varied presentations. © 2016,pakistan medical association. all rights reserved.
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کلیدواژه
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Acute renal failure; IgG4-related disease; Retroperitoneal fibrosis; Ureteric obstruction
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آدرس
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department of medicine,division of nephrology,lahore, Pakistan, department of pathology,shaukat khanum memorial cancer hospital,lahore, Pakistan, department of rheumatology,lahore, Pakistan, department of urology,fatima memorial hospital,nur international university,lahore, Pakistan, department of medicine,division of nephrology,lahore, Pakistan, department of medicine,division of nephrology,lahore, Pakistan
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Authors
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