Steroid responsive encephalopathy in cerebral amyloid angiopathy: A case report and review of evidence for immunosuppressive treatment

Cerebral amyloid angiopathy (caa) is a common but often asymptomatic disease,characterized by deposition of amyloid in cerebral blood vessels. we describe the successful treatment of caa encephalopathy with dexamethasone in a patient with caa-related inflammation causing subacute progressive encephalopathy and seizures,which is an increasingly recognized subtype of caa. the two pathological subtypes of caa-related inflammation are described and a review of the literature is performed concerning immunosuppressive treatment of caa-related inflammation with special attention to its pathological subtypes. immunosuppressive therapy appears to be an appropriate treatment for caa encephalopathy. © 2010 kloppenborg et al; licensee biomed central ltd.