An unusual initial presentation of Proteus syndrome: Macrosyndactyly [Proteus sendromunun nadir görülen formu: Makrosindaktili]

Proteus syndrome is a complex disorder characterized by a wide variety of deformities including macrodactyly. in the present report,we present a case with complex macrosyndactyly in his hand. the patient was surgically treated. however,he admitted with lymphangiomas on his body during the follow-up period,leading to the diagnosis of proteus syndrome. this article discusses the differential diagnosis of proteus syndrome and the treatment methods used for macrodactyly along with the presentation of the case.