Orbital Rosai–Dorfman Disease in a fifty-eight years old woman

Rosai–dorfman disease (rdd) is rare and characterized by histiocytic proliferation and massive cervical lymphadenopathy. about 40% of patients have extra-nodal involvement. ophthalmic involvement is seen in 10% of cases. a case of orbital rosai dorfman disease in a 58 years old woman is presented here, who was misdiagnosed as orbital inflammatory disease initially. the patient did not respond to a course of oral prednisolone. then complete surgical excision of the mass was performed and the histopathological examination was consistent with a diagnosis of rdd.