recurrent dermatofibrosarcoma protuberans of the vulva: a rare occurrence and review of literature

Objective: dermatofibrosarcoma protuberans (dfsp) of the vulva is an uncommon soft tissue tumor with fewer than 60 cases reported previously. distant metastasis is rare with a high propensity for local invasion. surgical management is the gold standard with adequate margin excision to prevent future recurrences. we report a case of vulvar dfsp requiring three resections to achieve primary clearance. to the best of our knowledge, this is the first case report from india. case report: a 35 years old female, presented with nodular vulvar mass for the third time arising from the upper part of right labia majora for the last year. she had a history of two similar episodes in the past for which excision was done and histopathology confirmed dfsp. the third wide local resection was performed with 3 cm margins and the margins were sent for intraoperative frozen section analysis, which was confirmed clear by the pathologist. the patient has been free of recurrence for two years. conclusion: dfsp is a challenging condition presenting as a nontender nodular mass characterized by local invasion and recurrence. early diagnosis and appropriate management using wide local excision with accurate margin assessment can achieve optimal results and prevent future recurrences.