an unusual case of genital lesion: a vulvar syringoma

Objective: syringoma is a benign adnexal neoplasm of sweat gland, usually presenting as extra-genital lesions, while vulvar localization is rare. moreover, syringoma is an uncommon vulvar neoplasms. case report: a 44-year-old woman with previous diagnosis of duodenal gastrointestinal stromal tumour, underwent a local surgical excision for an isolated, painful, vulvar lesion. the specimen was submitted for histological examination. a vulvar syringoma was diagnosed. conclusion: we describe this case according on its rarity and atypical presentation as well; therefore, vulvar neoplasms encompass many differential diagnoses, among which the incidence rate of syringoma is very low. although its rarity, syringoma should be included among the differential diagnosis for vulvar neoplasm.