Primitive Neuroectodermal Tumor, a Rare Cause of Musculoskeletal Manifestations in a Child

Among small blue round cell tumors, primitive neuroectodermal tumors (pnets) are a group of ewing sarcoma family of tumors that are highly aggressive, poorly differentiated and form a group of tumors defined by their appearance that are thought to derive from postganglionic parasympathetic primordial cells located throughout the parasympathetic autonomic nervous system. batsakis et al divided pnet family of tumors into the following 3 groups based on the tissue of origin: peripheral pnet, cns pnet and neuroblastoma.