Pigmented Epithelioid Melanocytoma in a Child: Unusual Clinical Presentation

Zembowicz et al coined the term pem for a “low-grade melanocytic tumor with metastatic potential indistinguishable from animal-type melanoma and epithelioid blue nevus”. pem is a distinct melanocytic tumor occurring in a sporadic setting and in the context of carney complex. a 10 year-old child was referred for evaluation of a blue-black cutaneous macule found in the right pectoral region. the lesion measured 0.4×0.3 cm. the histology of the lesion showed a densely pigmented dermal nodule with infiltrative borders. the proliferation was composed of epithelioid and spindle melanocytes with heavy pigmentation; atypical cells were present.