Congenital Embryonal Rhabdomyosarcoma with Prenatal Onset

Objective: rhabdomyosarcoma (rms) is the single most common type of soft tissue sarcoma in children and adolescents but it is extraordinarily rare in neonates. extremity rms comprises 20% of all sites, occurs more commonly in the leg than in the arm and accounts for 9% of all rms cases.case presentation: according to our review, this is the second case of rms on day one of life with congenital, antenatal feature, and postnatal progressive clinical course of a large tumor of the hand (pre-treatment staging t2bn1m0) with embryonic histological subtype and unfavo rable prognosis. the patient is a term newborn boy with huge mass in the right hand and palpable lymph node in subaxillar region.conclusion: congenital embryonal rhabdomyosarcoma is a rare form of sarcomas with congenital in nature, .antenatal feature and post natal progressive clinical course of sarcomas of extremities in newborn infants.