persistent truncus arteriosus with intact ventricular septum: clinical, hemodynamic and short-term surgical outcome

Introduction: truncus arteriosus with intact ventricular septum is a rare and unique variant of persistent truncus arteriosus (pta) which usually presents with central cyanosis and congestive heart failure in neonate and early infancy. associated cardiac and non-cardiac anomalies may affect morbidity and mortality of these patients. case presentation: we describe clinical presentation, echocardiography and angiographic features of a 7-month old boy with pta and intact ventricular septum who underwent surgical repair of the anomaly at our institution. operative findings, surgical procedure and short-term outcome are reported. conclusions: while our patient had systemic pulmonary arterial pressure at the time of complete surgical repair, it was improved after surgery.