outcome of multi-cystic dysplastic kidneys in children

Background: renal cystic diseases are important causes of chronic kidney disease (ckd). objectives: we report the pattern of renal cystic disease in children and evaluate the outcome of children with multicystic dysplastic kidney (mcdk). patients and methods: retrospective study of all children with cystic kidney diseases at king abdulaziz university hospital from 2006 to 2014. results: total of 55 children (30 males); 25 mcdk, 22 polycystic kidney diseases (pkd), 4 nephronophthises and 4 renal cysts. consanguinity was positive in 96.2%. mcdk and simple renal cyst patients had good renal function while pkd and nephronophthisis developed renal impairment. most mckd were diagnosed ante-natally, 16 of them were followed up for 3.4 (1.97) year. their last creatinine was 33.9 (13.5) umol/l. mcdk was spontaneously involuted at mean age of 2.6 (1.3) years in 56%. conclusions: mcdk is the commonest cystic renal disease and diagnosed ante-natally in the majority of cases. it has a good prognosis.