External Ocular Manifestations in Autosomal Dominant Dystrophic Epidermolysis Bullosa; a Case Report

Purpose: to present a case of autosomal dominant dystrophic epidermolysis bullosawith symblepharon formation due to eye rubbing.case report: a 10-year-old girl suffering from blistering and ulcerative lesions of thetrunk and palms and dystrophic nails since childhood was referred to our clinic with asymblepharon connecting the medial portion of the right upper lid to the super onasalquadrant of the cornea. the central cornea in both eyes exhibited mild subepithelialopacification. she had history of eye rubbing due to foreign body sensation in the righteye, resulting in red eye and blister-like conjunctival lesions since three years ago. shehad previously undergone surgical symblepharon removal leading to more severe recurrence of the condition.conclusion: dominant dystrophic epidermolysis bullosa may be accompanied byexternal ocular manifestations. protection of the eye from minor trauma such as rubbing may help prevent ocular complications.