Orbicularis oculi myectomy as a treatment for blepharospasm in a case of Schwartz Jampel syndrome

Purpose: to describe a patient with schwartz jampel vel aberfeld syndrome (sjs) who underwent orbicularis oculi myectomy as a treatment for blepharospasm. case report: a 4-year-old child with sjs did not respond to an injection of a single dose of botulinum toxin after one month,so orbicularis myectomy was then performed under general anesthesia. during the procedure,orbicularis vermiform movements were a useful guide for the extent of myectomy that the patient needed. he responded very well to this procedure and experienced significant relief of blepharospasm documented in follow-up visits for up to 6 months. conclusion: blepharospasm in patients with sjs can be treated with orbicularis oculi myectomy as a good functional method with faster and durable response in comparison to botulinum toxin injection. © 2016 journal of ophthalmic and vision research.