extensive aplasia cutis congenita: a case report

Aplasia cutis congenita (acc) is a rare congenital disorder characterized by localized or widespread skin absence. the most common site is the scalp and the main cause is unknown. here we report a case of extensive acc with scalp involvement. a female infant with an apgar score of 9 and weighing 3406 gr was born by cesarean section in besat hospital, sanandaj, iran. a lesion measuring 5×10 cm with highly prominent vessels was on the forehead and parietal bone without scalp, skull, or bone tissue leading to the brain tissue being covered with a thin membrane. other clinical examinations were normal. the newborn suffered from a ruptured aneurysm and intracerebral hemorrhage and underwent pharmacologic treatment. she died after 21 days of hospitalization. in order to prevent mortality in infants with skin defects, infection control is a priority. antibiotics could be administered in cases with extensive lesions to prevent neonatal sepsis and improve scar tissue formation. moreover, restorative measures should be taken if necessary.