Malignant giant cell tumor of soft parts in lumbosacral region

Giant cell tumor of soft parts is a rare neoplasm that mainly affectsadulst and the elderly and is usually located in the extremities. here we report achild with giant cell tumor of soft tissue, which is a very rare condition in childhood.clinical presentation: a 5 year old girl presented with a 5 month history of leftlower extremity pain. she had developed paraplegia before admission. onexamination, mild left lumbosacral swelling and tenderness was found. abdominaland pelvic ct-scan revealed an expansile lytic lesion of the left side of sacrum withsignificant soft tissue component extending toward the left iliac bone. lumbar mrirevealed a space occupying lesion originating from posterior l5 elements, projectingtoward the l1.intervention: the patient underwent surgery. a firm epidural hemorrhagic tumor ofl5, s1, and s2 with no spinal cord involvement was found. partial tumor resection(measuring 3*1*0.5 cm in maximal diameter) and laminectomy was done.conclusion: primary giant cell tumors of soft tissue are distinctive, rare neoplasmsthat exhibit a wide clinicopathologic spectrum similar to osseous gcts and need tobe differentiated from other giant cell rich soft tissue tumors. recognition of thistumor is important due to its behavior as a low grade malignancy, but this cannot bepredicted and metastasis does occur rarely.