Primary Ewing’s Sarcoma/Primitive Neuroectodermal Tumor of of Kidney - a Diagnostic Dilemma

Among the group of small round cell tumors of kidney ewing’s sarcoma/pnet is a very rare entity which has aggressive clinical course. we report a case of renal mass in 24 years old male which was histologically diagnosed as small round cell tumor of kidney. arrangement of the malignant cell along with vascular network in a filigree pattern was suspicious for a diagnosis of ewing’s sarcoma/pnet which was confirmed by positivity of cd 99 immunohistochemically. thus careful histological observation and immunohistochemical stains can give the proper diagnosis of primary ewing’s sarcoma/pnet thus removing the diagnostic dilemma in the group of small round cell tumors.