an unusual type of choledochal cyst with huge dilation of extrahepatic bile duct from hilum to ampulla of vater; a case report and literature review

Introduction: choledochal cyst is a rare problem, defined as congenital dilatation of the biliary tract. there are five particular categories of choledochal cysts with some sub-types. the optimal management is removal of entire extrahepatic biliary system in addition to cholecystectomy and reconstruction by roux-en-y hepaticojejunostomy. case presentation:we reported a 25 years old patient with a giant choledochal cyst. this choledochal cystmaybelong to subtype 1a plus affecting the intrapancreatic portion of commonbile duct (cbd). the cyst was successfully resected without any complications. conclusions: intraoperative finding of choledochal cyst is very important, therefore, knowledge of potential presence of this rare disease and its management with respect to anatomical variations is very important for surgeons.