Partial Internal Biliary Diversion in Progressive Familial Intrahepatic Cholestasis: Introduction of a New Approach

Introduction: facilitation of biliary salts secretion represents the mainstay of treatment for progressive familial intrahepatic cholestasis (pfic). the purpose of this study was to introduce a new approach for the treatment of progressive familial intrahepatic cholestasis (pfic) to avoid ostoma.case presentation: an 11-year-old girl with the diagnosis of pfic underwent cholecystoappendicostomy with myotomy operation. because of anastomosis stricture, she was reoperated with cholecystojejunocolic anastomosis and intussuscepted valve surgery. she was followed for 9 months. despite disappointing outcomes of internal drainage with cholecystoappendicostomy, results of cholecystojejunocolic anastomosis with intussuscepted valve surgery were promising. discussion: the cholecystojejunocolic anastomosis with intussuscepted valve surgery could be considered as a forthcoming approach in the treatment of intrahepatic cholestasis.