Primary Pulmonary Vein Leiomyosarcoma: A Case Report

Primary leiomyosarcoma of the heart is extremely rare and found in about 0.2% of all cardiactumors. here in a 26-year-old man with progressive dyspnea, which had started since 2 monthsago, is presented. echocardiography revealed a left atrial mass, which was suggestive for a atrialmyxoma.on the surgery, a tumoral tissue in the left atrium and pulmonary veins with attachmentto peripheral soft tissue, was seen and incompletely resected. histologic examination exhibited ahypercellular,necrotic and mitotically active spindle-celled tumor with fascicular arrangement.immunohistochemistry showed a positive reaction to sma in tumoral cells. the patient was advisedto refer for postoperative chemotherapy, which was rejected. one year later, the patient was broughtto hospital with tumor recurrence. chemotherapy was initiated for the patient immediately, but thepatient was expired 3 days later.