Ewing’s Sarcoma of Hand

Ewing’s sarcoma (es) is a highly malignant neoplasm of childhood and adolescence seen commonlyin both axial and appendicular skeleton but uncommonly in acral region. ewing’s tumor in thehand is extraordinarily rare. radiological features are variable and can mimic other commonlesions. we present a case of 13 year old female, with complaints of pain and swelling in righthand, which on x-ray showed periosteal reaction, giving a sun burst appearance and provisionaldiagnosis of osteosarcoma was made. the patient was operated and histopathological diagnosis ofes was confirmed. histopathological examination remains the mainstay of diagnosis, supportedby immunochemistry and cytogenetic studies. surgical extirpation with chemotherapy is thetherapeutic regimen of choice. we intend to report this case, because it is very rare location and theradiological features can mimic other lesions which commonly occur in this location like chronicosteomyelitis so it can be easily missed especially at preliminary evaluations.