Primary Leiomyosarcoma of the Kidney:A Case Report and Review of Literature

Primary sarcomas of the kidney are exceptional. among renal sarcomas, leiomyosarcoma is themost common histologic subtype amounting to 50-60% of all cases. the tumor usually arises fromeither the renal capsule or smooth muscle tissue in the renal pelvic wall. in this paper, we reporta patient with leiomyosarcoma of the kidney presented with non-specific abdominal pain and apalpable mass. histologic examination revealed a mesenchymal tumor composed of pleomorphicspindle cells arranged in interlacing pattern with high mitotic activity. immunohistochemical studywas positive for demin, smooth muscle actin (sma), and muscle specific antigen (msa).the rarityof this disease and very little information about it, its severity, and poor prognosis, uncommon formof presentation, large size of the mass, and difficulty in management are highlighted and reported.