Fahr’S Syndrome

Fahr’s syndrome is a rare neurodegenerative disorder. bilateral basal ganglia and dentate nuclei of the cerebellum are involved in this disorder and deposition of calcium is the hallmark of this syndrome. it has been recognized as a sporadic or inherited disease with variable presentations. in this article, we report a 40-year-old man with incidentally discovered brain calcification as the sole manifestation of fahr’s syndrome. a 40-year-old male without any comorbidities was presented with brain calcification that was found incidentally. brain imaging revealed symmetric calcifications in bilateral basal ganglia, internal capsules, and cerebral white matter. this pattern of calcification is highly suspicious of fahr’s syndrome. other pathologic processes that could lead to intracranial calcification were excluded. we present a young patient with sporadic and asymptomatic fahr’s syndrome after ruling out abnormalities of known calcium metabolism and developmental defects.