Clinical patterns of retinitis pigmentosa with special reference to maculopathy (A hospital based study)

Aim: to describe clinical patterns of retinitis pigmentosa with special emphasis on optical coherent tomographic picture of maculopathy. study period and design: 2010 to 2014 descriptive,retrospective study. methods: we retrospectively reviewed ninety seven patients of retinitis pigmentosa (rp),presenting in two different centers of lahore. the medical charts were analyzed. the data considered for the study was age,sex,ocular signs,symptoms,macular status and associated systemic problems of the patients. optical coherent tomography was used where pattern of maculopathy was not discernable clinically. the patients were divided into three age groups (≤ 19 years,20 to 40 years,>40 years). clinical patterns were compared among three groups. results: the age range was from 1 to 75 years (mean 29.34). male to female ratio was 1.2: 1. family consanguinity was positive in 70.10 % of patients. the initial clinical presentation was night blindness in 89.7 % patients. intra ocular pressures were normal in all cases. commonest ocular finding other than typical triad of rp was posterior vitreous detachment (pvd). usher syndrome was the commonest systemic association. maximum number of patients had typical rp. atrophic maculopathy had largest percentage in all groups.