Lung metastasis in primary cutaneous adenoid cystic carcinoma – Clinicopathological evaluation of a rare case with review of literature

Primary cutaneous adenoid cystic carcinoma (acc) is an extremely rare and indolent cutaneous malignancy with very infrequent distant metastasis. we present a case of primary cutaneous acc with bilateral lung metastases in a 57-year-old male along with literature review. to the best of our knowledge this is the tenth case of primary cutaneous acc reported presenting with distant metastasis. © 2017 national cancer institute,cairo university