Sturge Weber Syndrome--unusual presentation.

Sturge weber syndrome or encephalo-trigeminal angiomatosis is non-hereditary,congenital and rare disorder of unknown aetiology. it is characterised by vascular malformation with capillary venous angiomas involving face,eye and leptomeninges resulting in neurological and orbital manifestations. a case of 23 years old female presented with history of tonic-clonic convulsions,evidence of port wine stain on face since birth,characteristic ct findings diagnosed as a case of sturge weber syndrome is reported here for its rarity.