anesthesia management in rare case: cutis laxa syndrome

Cutis laxa is rare and heterogeneous group of disorders related to abnormalities in elastic tissue. it may be autosomal recessive, autosomal dominant, x linked or acquired. acquired cutis laxa has developed after a febrile illness, inflammatory skin disease such a lupus erythematosus or erythema multiform, amyloidosis, hypersensitivity reaction to penicillin and in infants born from women who were taking penicillamine. patients with cutis laxa have facial features, pulmonary emphysema, cor-pulmonale, and right-sided heart failure. we present a case with cutis laxa undescended testis, and mild pulmonary stenosis.