jervell-lange nielsen syndrome: a case report

There is a rare genetic disorder called jervell-lange nielsen syndrome that leaves people congenitally deaf and with a long qt interval. this can lead to deadly heart rhythm problems and sudden death. for the treatment of hearing loss, cochlear implants, and for the treatment of heart difficulties, beta-blockers, and in certain circumstances, implantable cardioverter defibrillators, arrhythmias, syncope attacks, and sudden death are recommended. we discuss the case of an 8-year-old child who was referred for cochlear implantation after being diagnosed with jervell-lange nielsen syndrome. in this study, we want to deal with patient management preoperatively and during surgery and describe the side effect of this syndrome.