Anesthetic management of hereditary methemoglobinemia [Kalitsal methemoglobinemide anestezi yönetimi]

Methemoglobinemia is a severe clinical disorder characterized with cyanosis and respiratory insufficiency resulting from decreased oxygen carrying capacity to the tissues because of the increased blood level of methemoglobin. methemoglobinemia is mostly an acquaired disorder which appears after toxic exposition; however rarely it is hereditary. in this study,anestesia management of a patient with hereditary methemoglobinemia who has undergone a thyroidectomy is presented as a case report. using higher concentrations of oxygen because of the decreased oxygen carrying capacity,using co-oxymeter instead of pulseoxy meter for determining peripheral oxygen saturation and avoiding oxydative agents are some of the perioperative precautions that should be taken in congenital methemoglobinemia.