Anesthesia for a case with bardet-biedl syndrome and application of postoperative nurse controlled analgesia [Bardet-bi̇edl sendromlu olguda anestezi̇ ve postoperati̇f hemşi̇re kontrollü analjezi̇ uygulamasi]

Bardet biedl syndrome (bbs) is a rare,autosomal recessive disease characterized by cone-rod dystrophy,truncal obesity,postaxial polydactyly,mental retardation,male hypogonadotrophic hypogonadism,complex female genitourinary malformations,and renal dysfunction. the perioperative period may be hazardous for these patients. anesthetic difficulties may be anticipated due to age,obesity,renal and hepatic dysfunction and mental retardation. in the present case report we aimed to share our general anesthesia management and the practice of nurse controlled analgesia techniques for postoperative analgesia for the vaginoplasty surgery of a child patient with bbs.