Lymphatic dysplasia syndrome with chylothorax: a case report

Lymphedema is a disease that is caused by the blockage of flow of lymph and is generally characterized with swelling (edema) in the extremities. primary lymphedema which is rarely seen can develop either at birth or symptoms can begin at puberty and is known as lymphedema praecox. lymphedema praecox is the most common form of primer lymphedema and is diagnosed by the exclusion of secondary causes. lymphatic dysplasia syndrome is defined as primary lymphedema with effusion in the third spaces of the body such as the pleura, pericardium and peritoneum. in this article, we present a rare case of a 14 year old girl who was diagnosed with lymphedema praecox/lymphatic dysplasia syndrome because she had edema in both her lower extremities and chylothorax in her right lung.