Papillon lefevre syndrome with multidisciplinar approach: 6 years follow–up

This paper presents treatment planning and 6 years follow–up of a patient with papillon lefevre syndrome (pls). papillon lefevre syndrome is a rare autosomal recessive syndrome characterized by palmoplantar hyperkeratozis and premature tooth loss. as a result of clinical, immunological and hematological findings, the patient referred to our department in 2005,was diagnosed as pls. the preliminary phase of the treatment consisted of extraction of all primary teeth under general anaesthesia. following the edentulous period, a removable denture was delivered. the denture was modified as permanent teeth erupted. additively, removal appliance with distal screw was applied. the patient is still under maintenance.