CONGENITAL INSENSITIVITY-TO-PAIN WITH ANHIDROSIS (CIPA): A CASE REPORT

Congenital sensitivity to pain and anhidrosis (cipa), appear in early childhood, is quite rare, autosomal recessive disorder characterized by insensitivity to pain is an autonomic neuropathy. in all cases there is no sensation of pain from birth. systemic anhydrous, eye dryness, lack of sweating, lack of pain in the extremities and mental retardation are the typical signs of the syndrome. the 8-year-old male patient having congenital insensitivity to pain syndrome, was admitted to dokuz eylul university faculty of medicine children's dental clinics with complaints of injuries in his tongue. during the oral examination; an extreme bite wound with excessive bleeding on the right side of the language determined. upper right 1st. and 2nd primary molars extracted in order to prevent the patient's tongue biting. in this study we aimed to present cipa; hereditary, sensory and autonomic neuropathy (hsan) known as type 4.