DENTAL TREATMENT APPROACH IN PEDIATRIC PATIENT WITH ECTODERMAL DYSPLASIA : A CASE REPORT

Ectodermal dyplasia is a hereditary disease associated with abnormal development of two or more embryonic ectodermal structures such as teeth, nail, hair, nerve cells and sweat glands. according to the state of sweat glands involvement ectodermal dysplasia is divided into two major grups: hydrotic and hypohydrotic/ anhydrotic. as hypohydrotic type is inherited in x- linked mode, hydrotic type is inherited in autosomally dominant. the most common oral manifestation of ectodermal dysplasia is teeth deficiency in primary and/ or permenant dentition. therefore, during the development of the child, protetic rehabilitations could be necessary. hydrotic type of ectodermal dysplasia diagnosed case with the typical features of the diseas such as hypodontia and onycodysplasia is presented in this study in term of oral manifestation and dental treatment approach.