Complex Ebstein’s anomaly in an 86-year-old Iranian man: A case report

Ebstein’s anomaly is defined as the significant apical displacement of the tricuspid valve causing tricuspid regurgitation. although a variety of concomitant lesions have been previously described,we herein introduce an unusual presentation. our patient was an 86-year-old man with a primary presentation of typical chest pain in the setting of recently diagnosed coronary artery disease with concomitant ebstein’s anomaly. we found mild-to-moderate tricuspid regurgitation,bicuspid aortic valve,persistent left superior vena cava,and patent foramen ovale. the patient had suffered from chest discomfort on exertion for 2 months with good functional capacity prior to diagnosis. coronary angiography revealed two-vessel disease. the patient refused surgery. he was treated with medical anti-ischemic therapy. he had good exercise tolerance with relief of chest pain at the latest follow-up. the features demonstrated in this case report suggest that there may be several adult survivors of complex congenital heart diseases requiring individualized surgical treatment plans. © 2017,tehran heart center. all rights reserved.