an unusual presentation of granulomatosis with polyangiitis

The granulomatosis with polyangiitis (gpa), formerly known as wegener’s granulomatosis, is a pauci-immune vasculitis involving small- and medium-sized blood vessels. classically, the patients inflicted with this disease present with a triad of necrotizing granulomatous inflammation of the respiratory tract, cutaneous necrotizing vasculitis, and glomerulonephritis (gn). the antinuclear (ana) and anti-neutrophil cytoplasmic antibodies (anca) are considered as relatively specific markers of the disease. herein, we presented the case of a patient who initially presented with sepsis but did not respond to the conventional antibiotics and later diagnosed with gpa.