Cor Triatriatum Sinistrum Presenting as Cyanotic Congenital Heart Disease A Rare Case Report

Cor triatriatum is an acyanotic congenital heart disease. we present a rarecase of cor triatriatum sinistrum in a 6-month-old female infant who waspresented with cyanosis and failure to thrive. the 2d transthoracicechocardiography and the doppler color flow imaging showed a proximalvenous chamber communicating to the distal left atrium throughrestrictive opening to the low-pressure, distal left atrial chamber.the saline contrast echocardiography confirmed a right-to-left atrialshunt due to a minor atrial septal defect. the defect was caused by apersistent pulmonary hypertension which had raised the right atrialpressure in the infant.to the best of our knowledge, barely any such cases have been reported inthe literature so far. our report highlights the clinical utility of the salinecontrast echo in other cases of congenital heart diseases.