isolated right ventricular non-compaction in a neonate born to a mother with gestational diabetes: a case report

Background: ventricular non-compaction, which is a rare congenital cardiomyopathy, results from an arrest in normal endomyocardial embryogenesis. it is characterized by a pattern of prominent trabecular meshwork and deep inter-trabecular recesses. the clinical manifestations include systolic and diastolic dysfunctions, heart failure, ventricular arrhythmias, and cardioembolic events. case report: here we present the case of a neonate (38 weeks, weighing 2580 gr) born to a mother with gestational diabetes (gdm) with isolated right ventricular non-compaction (irvnc) and systolic and diastolic right heart dysfunction due to meconium aspiration syndrome and tension pneumothorax. a 4-month follow-up demonstrated a complete improvement in the newborn. conclusion: it is of paramount importance to consider rvnc cardiomyopathy a differential diagnosis of cyanosis and respiratory distress due to meconium aspiration syndrome in neonate s born to mothers with gdm. apart from rv cardiac dysfunction, rvnc could cause such complications as pulmonary hypertension and tension pneumothorax. it can be also spontaneously improved in gmd.