temperature-sensitive recurrent, reversible auditory neuropathy in two iranian siblings

Two sibling cases with a temperature-sensitive form of auditory neuropathy from a consanguineous marriage of iranian descent have been described. they complained about the temporary loss of hearing and compromised speech comprehension after a slight fever or elevating the body temperature by vigorous exercises. a series of tests including brain mri, pure-tone audiometry, speech audiometry in quiet and noise, tympanometry, reflexometry, teoaes, cochlear microphonic, and abr were performed in a 24-hours interval at both febrile and afebrile states, and results are reported here. this report is the first example of temperature-sensitive auditory neuropathy in this geographical region.