Congenital Sensory Neuropathy as a Differential Diagnosis or Phagocytic Immunodeficiency

There are few reports about congenital indifference to pain or hereditary and sensoryautonomic neuropathy (hsan). several investigations for pathophysiology of thissyndrome have been performed and different classifications about it. in this report wepresent a case of hsan type ii with general absence of pain and self amputations andleprosy–like damage of extremities which was suspected to be phagocytic immunodeficiencydue to past history of repeated ulcer and abscess formation.