Crohn's Disease and Idiopathic Thrombocytopenic Purpura in a Patient with Ectodermal Dysplasia and Immunodeficiency

In this case report we will describe a rare association between anhyrotic ectodermaldysplasia (aed) and immunodeficiency and autoimmunity [in our case: idiopathicthrombocytopenic purpura (itp) and crohn disease]. aed is a rare congenital disordercharacterized by sparse hair, abnormal teeth and anhidrosis due to lack of eccrine glands.the survey of 87 cases with (aed) revealed only one irrirahle bowel disease (led). aedhas only two relevancies with immunodeficiency: (eda-id: ectodermal dysplasiaanhyrotic with immunodeficiency) and ape-ced (autoimmune polyendocrinopathy,candidiasis and ectodermal dysplasia) that in our case eda-id is strongly suspected