Primitive Neuroectodermal Tumor of the Kidney in a 22-Year-Old Male: A Rare Entity

Primitive neuroectodermal tumors of the kidney are rare tumors representing about1% of all sarcomas. extraskeletal primitive neuroectodermal tumors may be found inthe genitourinary tract, the testes, ovaries, uterus, or pancreas. renal primitive neuroec-todermal tumors are frequently aggressive and almost 30% of all newly diagnosed casespresent with distant metastases. surgical intervention, intensive chemotherapeuticdrugs and radiation therapy are the best choices for management.we discuss the case of a 22-year-old male who presented with a left renal mass. heunderwent nephrectomy followed by histopathological examination. microscopic andimmunohistochemical examination revealed a primitive neuroectodermal tumor.