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Epidermal Nevus Syndrome and Dysplatic Kidney Disease
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نویسنده
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Nickavar Azar ,Atefi Najmessadat ,Kamyab Hesari Kambiz
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منبع
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acta medica iranica - 2014 - دوره : 52 - شماره : 8 - صفحه:647 -649
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چکیده
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Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. multicystic kidney disease has been very rarely reported in this syndrome. here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hemi hypertrophy, and multicystic dysplastic kidney complicated with wilms' tumor. according to this association, it is suggested to search for dysplastic kidney disease in patients with neurocutaneous disorders.
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کلیدواژه
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Epidermal nevus syndrome; Multicystic dysplastic kidney; Wilms' tumor; Neurocutaneous disease; Seizure
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آدرس
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iran university of medical sciences, Ali-Asghar Children’s Hospital, Department of Pediatric Nephrology, ایران, iran university of medical sciences, Aliasghar Children's Hospital, Department of Dermatology, ایران, tehran university of medical sciences tums, Razi Dermatology Hospital, Department of Pathology, ایران
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Authors
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