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A Case with Pachyonychia Congenita and B-cell Lymphoma
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نویسنده
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dos Santos Vitorino Modesto ,Loures Thiago Pereira ,Rego João Daniel Bringel ,Teixeira Christiane Aires ,de Carvalho Kayursula Dantas ,Nascimento Afonso Lucas Oliveira
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منبع
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acta medica iranica - 2014 - دوره : 52 - شماره : 7 - صفحه:578 -581
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چکیده
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Pachyonychia congenital (pc) is a rare autosomal dominant genodermatosis characterized hyperkeratosis affecting the nails and palmoplantar areas, oral leukokeratosis, and cystic lesions. a 39-yearold woman with pc type 1 (jadassohn-lewandowsky syndrome) and b-cell lymphoma is described. no similar disorders or parental consanguinity were found in her family. typical features of pc developed since her early childhood and the diagnosis of b-cell lymphoma was established seven years ago, without a clear causal relation between these entities. despite inherent limitations of a single case, this report may contribute to pc understanding.
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کلیدواژه
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Jadassohn-Lewandowsky syndrome; B-cell lymphoma; Pachyonychia congenita; Palmoplantar keratoderma
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آدرس
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Catholic University, Brazil. Armed Forces Hospital, Department of Internal Medicine, Brazil, Armed Forces Hospital, Department of Internal Medicine, Brazil, Armed Forces Hospital, Division of Pneumology, Brazil, Armed Forces Hospital, Division of Pneumology, Brazil, Armed Forces Hospital, Department of Internal Medicine, Brazil, Armed Forces Hospital, Department of Internal Medicine, Brazil
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Authors
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