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Familial Congenital Hepatic Fibrosis: Report of A Family With Three Affected Children
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نویسنده
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Farahmand Fatemeh ,Soleimani Khadije ,Hashemi Mojtaba ,Shafieyoun Arezoo ,Rezaei Nima ,Yousefi Azizollah
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منبع
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Acta Medica Iranica - 2013 - دوره : 51 - شماره : 9 - صفحه:655 -656
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چکیده
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Congenital hepatic fibrosis (chf) is a developmental disorder of the biliary system, characterized by defective remodeling of the ductal plate. herein a family of three children, from consanguineous parents, with minor thalassemia is presented who suffered from congenital hepatic fibrosis (chf). prompt diagnosis and appropriate treatment are necessary to avoid further complications in the affected patients.
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کلیدواژه
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Autoimmune Hepatitis; Congenital Hepatic Fibrosis; Ductal Plate Malformation; Transjugular Intrahepatic Portosystemic Shunt
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آدرس
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Tehran University Of Medical Sciences Tums, Children'S Medical Center, Pediatrics Center Of Excellence, Department Of Pediatric Gastroenterology, ایران, Arak University Of Medical Sciences, Department Of Cardiology, ایران, Arak University Of Medical Sciences, Department Of Cardiology, ایران, Tehran University Of Medical Sciences Tums, Children'S Medical Center, Research Center For Immunodeficiencies, ایران, Tehran University Of Medical Sciences Tums, Children'S Medical Center, Research Center For Immunodeficiencies, School Of Medicine, Molecular Immunology Research Center, Department Of Immunology, ایران, Tehran University Of Medical Sciences Tums, Children'S Medical Center, Pediatrics Center Of Excellence, Department Of Pediatric Gastroenterology, ایران
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Authors
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