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Case for diagnosis
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نویسنده
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lima l.a. ,haddad n.c.m. ,lima r.b. ,d'acri a.m. ,martins c.j. ,sampaio f.m.s. ,gualberto g.v. ,de cerqueira f.g.m. ,de cerqueira a.m.m. ,treu c.m. ,vargas t.j.s. ,leyva a.m. ,husein-elahmed h. ,aneiros-fernandez j. ,almodovar-real a. ,ruiz-carrascosa j.c.
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منبع
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journal brazilian annals of dermatology - 2014 - دوره : 89 - شماره : 3 - صفحه:521 -522
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چکیده
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Degos disease,also known as malignant atrophic papulosis,is a rare occlusive vasculopathy of unknown etiology characterized by infarcts in the dermis,gastrointestinal tract,central nervous system,and other organs. it is characterized by papules,which become umbilicated and evolve with a depressed porcelainwhite central area,with an erythematous halo with telangiectasias. histological findings include wedge-shaped dermoepidermal necrosis and blood vessel thrombosis. approximately 50-60% of patients with systemic symptoms die within 2-3 years,most due to gastrointestinal perforation. we report a typical case,with lethal outcome,in a 45-year-old woman. © 2014 by anais brasileiros de dermatologia.
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کلیدواژه
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Complement C5; Malignant atrophic papulosis; Vascular diseases
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آدرس
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universidade federal do estado do rio de janeiro (unirio),rio de janeiro (rj), Brazil, universidade federal do estado do rio de janeiro (unirio),rio de janeiro (rj), Brazil, universidade federal do estado do rio de janeiro (unirio),rio de janeiro (rj), Brazil, universidade federal do estado do rio de janeiro (unirio),rio de janeiro (rj), Brazil, universidade federal do estado do rio de janeiro (unirio),rio de janeiro (rj), Brazil, hospital federal de bonsucesso (hfb),rio de janeiro (rj), Brazil, hospital federal de bonsucesso (hfb),rio de janeiro (rj), Brazil, universidade gama filho (ugf),rio de janeiro (rj), Brazil, hospital municipal jesus,rio de janeiro (rj), Brazil, policlínica geral do rio de janeiro (pgrj),rio de janeiro (rj), Brazil, hospital federal de bonsucesso (hfb),rio de janeiro (rj), Brazil, university hospital - granada, Spain, cabra hospital - cordoba, Spain, university hospital - granada, Spain, university hospital - granada, Spain, university hospital - granada, Spain
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Authors
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