|
|
|
|
Segmental Darier’s disease: A presentation of difficult diagnosis
|
|
|
|
|
|
|
|
نویسنده
|
medeiros p.m. ,alves n.r.m. ,trujillo j.m. ,da silva c.c. ,de faria p.c. ,da silva r.s.
|
|
منبع
|
journal brazilian annals of dermatology - 2015 - دوره : 90 - شماره : 3 - صفحه:S62 -S65
|
|
چکیده
|
Darier’s disease is a rare autosomal dominant genodermatosis. it has an estimated prevalence of 1 in 55,000 to 100,000 individuals,regardless of gender. it is characterized by multiple keratotic papules on the seborrheic areas of the trunk,scalp,forehead and flexures,and the clinical picture is worsened by heat,sun exposure,perspiration and mechanical trauma. histopathology observed loss of epithelial adhesion and abnormal kerati-nization. about 10% of cases present in the localized form of the disease. we report a case of segmental darier’s disease type i and discuss the main characteristics of this condition. © 2015 by anais brasileiros de dermatologia.
|
|
کلیدواژه
|
Darier’s disease; Mosaicism; Skin diseases; Skin diseases genetic
|
|
آدرس
|
universidade do estado do rio de janeiro (uerj),rio de janeiro, Brazil, universidade do estado do rio de janeiro (uerj),rio de janeiro, Brazil, universidade do estado do rio de janeiro (uerj),rio de janeiro, Brazil, universidade do estado do rio de janeiro (uerj),rio de janeiro, Brazil, universidade do estado do rio de janeiro (uerj),rio de janeiro, Brazil, universidade do estado do rio de janeiro (uerj),rio de janeiro, Brazil
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
Authors
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|
|