Porokeratotic eccrine and hair follicle nevus: A report of two cases and review of the literature

Porokeratotic eccrine and hair follicle nevus is a very rare non-hereditary disorder of keratinization with eccrine and hair follicle involvement with only 9 cases described in the literature. in 2009 the term porokeratotic anexial ostial nevus was proposed to comprehend porokeratotic eccrine and hair follicle nevus and a related and more common process without follicular involvement: porokeratotic eccrine ostial and dermal duct nevus recent findings suggest that both entities may be produced by a mutation in gjb2 gene,which is associated to kid syndrome. herein we report 2 cases of porokeratotic eccrine and hair follicle nevus and review the existing cases in the spanish and english literature. © 2017 by anais brasileiros de dermatologia.